Dermatofibrosarcoma protuberans in a 52years old man: A case report
Keywords:
Fibroma, dermatofibroma, fibrosarcoma, soft tissue sarcoma, Fibrous HistiocytomaAbstract
Background
Dermatofibrosarcoma Protuberans (DFSP) is categorized as a skin tumour by WHO recent classification. It is slowing growing, nodular neoplasm of intermediate grade malignancy that is found almost exclusively in the dermis from which it often invades the subcutaneous tissue. Most cases are seen mainly in adulthood but it can also be seen in childhood. They are commoner in blacks, usually found on the trunk and as a group they are usually much larger than Dermatofibromas.
Case Presentation
We present the case of a 52years old retired driver with a 29years history of recurrent facial tumour. Has had excision 14 times in various hospitals prior to presentation to us. He sustained facial trauma from a fall while trying to collect water from a well some months prior to the growth of the first tumour. At presentation we found a middle aged man with multiple facial tumours, multiple facial scars, nasal dorsum deviation with reduced patency. He had various investigations done, which include computerized tomographic scan of the paranasal sinuses and brain that showed no brain, bone or sinuses affectation. Excision biopsy was done and histology report was that of dermatofibrosarcoma protuberans.
Conclusion
In multiple recurrences with previous surgical scars, it may not be possible achieving a good margin during excision as noticed in our case. For such cases adjuvant radiotherapy is of benefit in preventing recurrence.
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